Oculocutaneous Albinism - Absence of a Fovea

These are SD-OCT images of the eyes of a 68 year old man with oculocutaneous albinism. His visual acuity had been 20/80 right, 20/100 left for years. He had high refractive error (R-+1.25+3.75X85 and L-+1.00+3.75X100) and used a +4.00 reading add and a Kindle with adjustable font size for reading as a low vision aid. He had always been light sensitive. He had nystagmus of both eyes. The iris showed iris transillumination defects. The fundus photographs are shown in the accompanying image found in this section of the website. The OCT images show no foveal depression in either eye (red arrows).