Congential Hypertrophy of the Pigment Epithelium Lesion

The OPTOS fundus photograph shown comes from a 10-year-old asymptomatic girl with pinhole visual acuity of 20/40 in the right eye and 20/32 in the left eye. The slit lamp exam was normal in both eyes. The fundus exam showed a 1.5 disc diameter outer retinal black lesion at 8 oÕclock turquoise arrow). It has a hypopigmented inferotemporal border. Its appearance is typical for congenital hypertrophy of the retinal pigment epithelium lesion. The left eye was normal. Aside from requiring a refractive correction, no treatment was recommended. The patient was reassured the lesion was benign with no malignant potential. She was asked to keep follow up visits with primary eye care provider and return as needed for retina evaluation.